Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001070336 | SCV001235559 | uncertain significance | Autosomal recessive severe congenital neutropenia due to CSF3R deficiency | 2024-11-11 | criteria provided, single submitter | clinical testing | This sequence change replaces tryptophan, which is neutral and slightly polar, with arginine, which is basic and polar, at codon 542 of the CSF3R protein (p.Trp542Arg). This variant is present in population databases (rs763748002, gnomAD 0.006%). This variant has not been reported in the literature in individuals affected with CSF3R-related conditions. ClinVar contains an entry for this variant (Variation ID: 863380). Invitae Evidence Modeling of protein sequence and biophysical properties (such as structural, functional, and spatial information, amino acid conservation, physicochemical variation, residue mobility, and thermodynamic stability) has been performed for this missense variant. However, the output from this modeling did not meet the statistical confidence thresholds required to predict the impact of this variant on CSF3R protein function. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Genetic Services Laboratory, |
RCV001819795 | SCV002072373 | uncertain significance | not specified | 2019-04-15 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV004977995 | SCV005562423 | uncertain significance | Inborn genetic diseases | 2024-07-09 | criteria provided, single submitter | clinical testing | The c.1624T>C (p.W542R) alteration is located in exon 13 (coding exon 11) of the CSF3R gene. This alteration results from a T to C substitution at nucleotide position 1624, causing the tryptophan (W) at amino acid position 542 to be replaced by an arginine (R). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |