Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Mayo Clinic Laboratories, |
RCV003480529 | SCV004227807 | uncertain significance | not provided | 2023-06-13 | criteria provided, single submitter | clinical testing | BP4 |
Labcorp Genetics |
RCV005100307 | SCV005847029 | uncertain significance | Autosomal recessive severe congenital neutropenia due to CSF3R deficiency | 2024-02-17 | criteria provided, single submitter | clinical testing | This sequence change replaces cysteine, which is neutral and slightly polar, with tyrosine, which is neutral and polar, at codon 770 of the CSF3R protein (p.Cys770Tyr). This variant is not present in population databases (gnomAD no frequency). This variant has not been reported in the literature in individuals affected with CSF3R-related conditions. An algorithm developed to predict the effect of missense changes on protein structure and function (PolyPhen-2) suggests that this variant is likely to be tolerated. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |