Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV003698858 | SCV004459927 | pathogenic | not provided | 2024-01-08 | criteria provided, single submitter | clinical testing | This sequence change creates a premature translational stop signal (p.Gln663*) in the GGCX gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in GGCX are known to be pathogenic (PMID: 17110937, 17327402, 24520408). This variant is not present in population databases (gnomAD no frequency). This variant has not been reported in the literature in individuals affected with GGCX-related conditions. ClinVar contains an entry for this variant (Variation ID: 992374). For these reasons, this variant has been classified as Pathogenic. |
Bioscientia Institut fuer Medizinische Diagnostik Gmb |
RCV001280813 | SCV001468152 | likely pathogenic | Vitamin K-dependent clotting factors, combined deficiency of, type 1 | 2020-06-17 | no assertion criteria provided | clinical testing |