Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000187697 | SCV000241294 | likely pathogenic | not provided | 2016-03-09 | criteria provided, single submitter | clinical testing | The V620M variant in the GRIN2B gene has not been reported previously as a pathogenic varaint nor as a benign polymorphism, to our knowledge. The V620M variant was not observed in approximately 6500 individuals of European and African American ancestry in the NHLBI Exome Sequencing Project, indicating it is not a common benign variant in these populations. The V620M variant is a conservative amino acid substitution, which is not likely to impact secondary protein structure as these residues share similar properties. This substitution is predicted to occur at a position within the cytoplasmic domain that is conserved across species. In silico analysis predicts this variant is probably damaging to the protein structure/function. Therefore this variant is likely pathogenic; however the possibility that is benign cannot be excluded. |
Hudson |
RCV000495871 | SCV000583966 | likely pathogenic | Intellectual disability, autosomal dominant 6; Developmental and epileptic encephalopathy, 27 | 2025-02-28 | criteria provided, single submitter | research | |
Institute of Human Genetics, |
RCV001172368 | SCV001335423 | likely pathogenic | Intellectual disability, autosomal dominant 6 | 2017-04-04 | criteria provided, single submitter | clinical testing | This variant was identified as de novo (maternity and paternity confirmed). |
Genome |
RCV001265244 | SCV001443358 | likely pathogenic | Complex neurodevelopmental disorder | 2018-02-02 | no assertion criteria provided | provider interpretation | Submission from Simons Searchlight facilitated by GenomeConnect. Variant interpreted by the Simons Searchlight team most recently on 2018-02-02 and interpreted as Likely Pathogenic. Variant was initially reported on 2014-05-12 by GTR ID of laboratory name 26957. The reporting laboratory might also submit to ClinVar. |