Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000413196 | SCV000492250 | likely pathogenic | not provided | 2016-12-09 | criteria provided, single submitter | clinical testing | A novel c.3006_3009dupGCTC variant that is likely pathogenic has been identified in the GRIN2B gene. The c.3006_3009dupGCTC variant has not been published as a pathogenic variant, nor has it been reported as a benign variant to our knowledge. The c.3006_3009dupGCTC variant is not observed in large population cohorts (Lek et al., 2016; 1000 Genomes Consortium et al., 2015; Exome Variant Server). The c.3006_3009dupGCTC variant in the GRIN2B gene causes a frameshift starting with codon Tyrosine 1004, changes this amino acid to an Alanine residue and creates a premature Stop codon at position 5 of the new reading frame, denoted p.Tyr1004AlafsX5. This variant is predicted to cause protein truncation as the last 481 amino acids of the GRIN2B protein are changed to 4 incorrect amino acids. Therefore, this variant is likely pathogenic; however, the possibility that it is benign cannot be excluded. |