Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000215391 | SCV000279698 | uncertain significance | not provided | 2015-12-14 | criteria provided, single submitter | clinical testing | The R1138L variant has not beenpublished as a pathogenic variant, nor has it been reported as a benign variant to our knowledge. It was not observedin approximately 6,500 individuals of European and African American ancestry in the NHLBI Exome SequencingProject, indicating it is not a common benign variant in these populations. The R1138L variant is a non-conservativeamino acid substitution, which is likely to impact secondary protein structure as these residues differ in polarity,charge, size and/or other properties. This substitution occurs at a position that is conserved across species. In silicoanalysis is inconsistent in its predictions as to whether or not the variant is damaging to the proteinstructure/function. Based on the currently available information, it is unclear whether this variant is a pathogenicvariant or a rare benign variant. |
Labcorp Genetics |
RCV001232895 | SCV001405467 | benign | Intellectual disability, autosomal dominant 6; Developmental and epileptic encephalopathy, 27 | 2023-10-13 | criteria provided, single submitter | clinical testing |