Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000658428 | SCV000780200 | uncertain significance | not provided | 2018-05-31 | criteria provided, single submitter | clinical testing | A variant of uncertain significance has been identified in the GRIN2B gene. The V156I variant has not been published as a pathogenic variant, nor has it been reported as a benign variant to our knowledge. The V156I variant is not observed in large population cohorts (Lek et al., 2016). However, the V156I variant is a conservative amino acid substitution, which is not likely to impact secondary protein structure as these residues share similar properties. In-silico analyses, including protein predictors and evolutionary conservation, support that this variant does not alter protein structure/function. Therefore, based on the currently available information, it is unclear whether this variant is a pathogenic variant or a rare benign variant. |
Labcorp Genetics |
RCV001296560 | SCV001485526 | uncertain significance | Intellectual disability, autosomal dominant 6; Developmental and epileptic encephalopathy, 27 | 2021-09-01 | criteria provided, single submitter | clinical testing | |
Genome |
RCV000844991 | SCV000986818 | not provided | GRIN2B-related disorder | no assertion provided | phenotyping only | Variant interpretted as Uncertain significance and reported on 05/31/2018 by GTR ID 26957. GenomeConnect assertions are reported exactly as they appear on the patient-provided report from the testing laboratory. GenomeConnect staff make no attempt to reinterpret the clinical significance of the variant. |