Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Eurofins Ntd Llc |
RCV000173172 | SCV000224265 | uncertain significance | not provided | 2014-11-07 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV000173172 | SCV003248088 | pathogenic | not provided | 2023-04-05 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. This variant has not been reported in the literature in individuals affected with IMPDH1-related conditions. This sequence change creates a premature translational stop signal (p.Gln25Serfs*29) in the IMPDH1 gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in IMPDH1 are known to be pathogenic (PMID: 14981049, 33090715). This variant is present in population databases (rs767123748, gnomAD 0.01%). |