Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001064687 | SCV001229600 | uncertain significance | not provided | 2022-10-05 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Algorithms developed to predict the effect of missense changes on protein structure and function (SIFT, PolyPhen-2, Align-GVGD) all suggest that this variant is likely to be disruptive. ClinVar contains an entry for this variant (Variation ID: 858742). This variant has not been reported in the literature in individuals affected with IMPDH1-related conditions. This variant is not present in population databases (gnomAD no frequency). This sequence change replaces glycine, which is neutral and non-polar, with alanine, which is neutral and non-polar, at codon 233 of the IMPDH1 protein (p.Gly233Ala). |
DBGen Ocular Genomics | RCV003389484 | SCV004101741 | pathogenic | Retinitis pigmentosa 10 | 2022-01-01 | criteria provided, single submitter | clinical testing | Class 5 ACMG Guidelines, 2015 |