Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Center of Excellence in Genomics and Precision Dentistry, |
RCV001807870 | SCV002058097 | likely pathogenic | Amelogenesis imperfecta type 1H | criteria provided, single submitter | clinical testing | The heterozygous splice site variant c.1661-3C>G in ITGB6 (NM_000888.5) was identified in a patient with autosomal recessive amelogenesis imperfecta who also harbored heterozygous nonsense mutation c.625G>T p.(Gly209Ter). The c.1661-3C>G variant was inherited from his unaffected father and predicted to cause alteration to WT splice acceptor site. This variant was classified as likely pathogenic by ACMG guidelines. |