Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Rajaie Cardiovascular, |
RCV003228861 | SCV003925665 | likely pathogenic | Andersen Tawil syndrome | criteria provided, single submitter | research | ||
Ambry Genetics | RCV004285631 | SCV005036752 | uncertain significance | Cardiovascular phenotype | 2024-03-13 | criteria provided, single submitter | clinical testing | The p.V200M variant (also known as c.598G>A), located in coding exon 1 of the KCNJ2 gene, results from a G to A substitution at nucleotide position 598. The valine at codon 200 is replaced by methionine, an amino acid with highly similar properties. This amino acid position is well conserved in available vertebrate species. In addition, this alteration is predicted to be deleterious by in silico analysis. Based on the available evidence, the clinical significance of this alteration remains unclear. |