Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Prevention |
RCV003974953 | SCV004791790 | benign | PRLR-related disorder | 2019-07-16 | criteria provided, single submitter | clinical testing | This variant is classified as benign based on ACMG/AMP sequence variant interpretation guidelines (Richards et al. 2015 PMID: 25741868, with internal and published modifications). |
OMIM | RCV000074480 | SCV000108565 | pathogenic | Multiple fibroadenoma of the breast | 2013-11-21 | no assertion criteria provided | literature only | |
Reproductive Health Research and Development, |
RCV000074480 | SCV001142344 | benign | Multiple fibroadenoma of the breast | 2020-01-06 | no assertion criteria provided | curation | NM_000949.5:c.508A>C (Ile170Leu) was reported as I146L in the literature. Bogorad et al. used multiple functional assays, which unambiguously converge to the evidence that I146L exhibits constitutive activity, highlighting the remarkable effect of this single substitution on the biological properties of the PrlR (PMID: 24195502). This variant has an allele frequency of 0.027 in European (non-Finnish) subpopulation in the gnomAD database, including 71 homozygous occurrences. Taken together, we interprete this variant as Benign/Likely benign variant. ACMG/AMP criteria applied: BS1, BS2, PS3. |