Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001934782 | SCV002127741 | pathogenic | Diamond-Blackfan anemia | 2021-10-02 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. This variant has not been reported in the literature in individuals affected with RPL11-related conditions. This variant is not present in population databases (ExAC no frequency). This sequence change creates a premature translational stop signal (p.Ser51Phefs*4) in the RPL11 gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in RPL11 are known to be pathogenic (PMID: 19061985, 19773262). |