Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV001574903 | SCV001801791 | uncertain significance | not provided | 2019-11-26 | criteria provided, single submitter | clinical testing | Not observed in large population cohorts (Lek et al., 2016); In silico analysis, which includes protein predictors and evolutionary conservation, supports a deleterious effect |
OMIM | RCV004699426 | SCV005201146 | pathogenic | SPASTIC PARAPLEGIA 93, AUTOSOMAL RECESSIVE | 2024-09-09 | no assertion criteria provided | literature only |