Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ce |
RCV003393324 | SCV004133167 | likely benign | not provided | 2023-02-01 | criteria provided, single submitter | clinical testing | ALG11: BP4 |
Women's Health and Genetics/Laboratory Corporation of America, |
RCV004690409 | SCV005185208 | uncertain significance | not specified | 2024-05-20 | criteria provided, single submitter | clinical testing | Variant summary: ALG11 c.646G>A (p.Gly216Arg) results in a non-conservative amino acid change located in the ALG11 mannosyltransferase, N-terminal domain (IPR031814) of the encoded protein sequence. Four of five in-silico tools predict a benign effect of the variant on protein function. The variant allele was found at a frequency of 8e-06 in 251246 control chromosomes. The available data on variant occurrences in the general population are insufficient to allow any conclusion about variant significance. To our knowledge, no occurrence of c.646G>A in individuals affected with ALG11-Congenital Disorder Of Glycosylation and no experimental evidence demonstrating its impact on protein function have been reported. ClinVar contains an entry for this variant (Variation ID: 2643824). Based on the evidence outlined above, the variant was classified as uncertain significance. |