Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Clin |
RCV004732494 | SCV005367878 | benign | Centronuclear myopathy | 2024-08-07 | reviewed by expert panel | curation | The variant NM_001005361.3:c.654C>T is a synonymous (silent) variant (p.Asp218=) in exon 5/21 of DNM2. The filtering allele frequency (the lower threshold of the 95% CI of 29/1180014) of the c.654C>T variant in DNM2 is 0.00001663 for European (non-Finnish) chromosomes by gnomAD v4.1, which is higher than the ClinGen Congenital Myopathies VCEP threshold (≥0.0000015) for BA1, and therefore meets this criterion (BA1). The c.654C>T (p.Asp218=) variant is a synonymous (silent) variant that is not predicted by SpliceAI to impact splicing. In addition, it occurs at a nucleotide that is not conserved as shown by UCSC Genome Browser (BP4, BP7). In summary, this variant meets the criteria to be classified as benign for autosomal dominant centronuclear myopathy based on the ACMG/AMP criteria applied, as specified by the ClinGen Congenital Myopathies VCEP: BA1, BP4, BP7. (ClinGen Congenital Myopathies VCEP specifications version 1; 8/7/2024) |
Labcorp Genetics |
RCV001492234 | SCV001696841 | likely benign | Charcot-Marie-Tooth disease dominant intermediate B | 2024-08-15 | criteria provided, single submitter | clinical testing | |
Gene |
RCV001549566 | SCV001769745 | likely benign | not provided | 2019-07-11 | criteria provided, single submitter | clinical testing |