Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV003190727 | SCV003873297 | uncertain significance | Inborn genetic diseases | 2023-01-17 | criteria provided, single submitter | clinical testing | The c.953G>A (p.R318Q) alteration is located in exon 8 (coding exon 6) of the RHBDF2 gene. This alteration results from a G to A substitution at nucleotide position 953, causing the arginine (R) at amino acid position 318 to be replaced by a glutamine (Q). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |
Baylor Genetics | RCV003466038 | SCV004209078 | uncertain significance | Palmoplantar keratoderma-esophageal carcinoma syndrome | 2023-06-02 | criteria provided, single submitter | clinical testing |