Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001937724 | SCV002179210 | uncertain significance | not provided | 2021-05-26 | criteria provided, single submitter | clinical testing | This variant has not been reported in the literature in individuals with NEXMIF-related conditions. This sequence change replaces glycine with arginine at codon 15 of the NEXMIF protein (p.Gly15Arg). The glycine residue is highly conserved and there is a moderate physicochemical difference between glycine and arginine. This variant is present in population databases (rs752877406, ExAC 0.002%), including at least one homozygous and/or hemizygous individual. Algorithms developed to predict the effect of missense changes on protein structure and function are either unavailable or do not agree on the potential impact of this missense change (SIFT: "Deleterious"; PolyPhen-2: "Benign"; Align-GVGD: "Class C0"). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |