Total submissions: 5
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Fulgent Genetics, |
RCV001280899 | SCV001752516 | pathogenic | Polycystic kidney disease, adult type | 2022-03-13 | criteria provided, single submitter | clinical testing | |
Gene |
RCV003166614 | SCV003915063 | uncertain significance | not provided | 2023-03-28 | criteria provided, single submitter | clinical testing | Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; This variant is associated with the following publications: (PMID: 17582161, 30333007, 31317121, 25340609, 27499327, 15775720, 22508176, 24694054, 31740684, 23431072) |
Juno Genomics, |
RCV001280899 | SCV005418264 | uncertain significance | Polycystic kidney disease, adult type | criteria provided, single submitter | clinical testing | PM2_Supporting+PS4_Moderate+PP4 | |
Ambry Genetics | RCV004960677 | SCV005475087 | uncertain significance | Inborn genetic diseases | 2024-07-11 | criteria provided, single submitter | clinical testing | The c.10948G>A (p.G3650S) alteration is located in exon 37 (coding exon 37) of the PKD1 gene. This alteration results from a G to A substitution at nucleotide position 10948, causing the glycine (G) at amino acid position 3650 to be replaced by a serine (S). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |
Bioscientia Institut fuer Medizinische Diagnostik Gmb |
RCV001280899 | SCV001468245 | pathogenic | Polycystic kidney disease, adult type | 2020-02-24 | no assertion criteria provided | clinical testing |