Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Molecular Genetics Laboratory, |
RCV004781990 | SCV005393881 | likely pathogenic | Polycystic kidney disease, adult type | 2024-11-07 | criteria provided, single submitter | clinical testing | This variant was detected in a female with polycystic kidney disease, visual abnormality and additional ribs. The segregation molecular genetic analysis in her parents was not performed. The relevant medical/scientific publications report on pathogenic PKD1 gene variants as a molecular cause of polycystic kidney disease 1 (PMID:10655152;8320707;2215575). This novel variant correlates with the clinical manifestation of PKD1. To conclude, the variant is classified as likely pathogenic (ACMG PVS1, PM2). |