Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Breda Genetics srl | RCV001293852 | SCV001482517 | likely pathogenic | Polycystic kidney disease, adult type | 2021-02-03 | criteria provided, single submitter | clinical testing | The variant c.290A>G (p.Asp97Gly) in the PKD1 gene is reported as likely pathogenic for the dominant form of polycystic kidney disease in the Global Variome shared LOVD database v.3.0 (genomic variant: #0000671281). The missense mutation c.290A>G (p.Asp97Gly) has been firstly reported by Hoefele et al. (2010) in a patient with autosomal dominant polycystic kidney disease (PMID: 21115670) and recently by Pandita et al. (2019) in a sporadic case of autosomal dominant polycystic kidney disease (PMID: 30816285). This variant has not been reported in dbSNP, gnomAD or ClinVar. The nucleotide position is conserved across 35 mammalian species (GERP RS: 4.17). In silico analysis indicates that the variant might be damaging. |