Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Genesis Genoma Lab, |
RCV003237325 | SCV003935201 | likely pathogenic | Polycystic kidney disease, adult type | 2023-06-26 | criteria provided, single submitter | clinical testing | This variant was detected in an 18 year old male with clinical diagnosis of polycystic kidney disease and positive family history. It is not reported in gnomAD database. Downstream frameshift mutations in PKD1 with pathogenic clinical significance was been reported in ClinVar database. |