Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Juno Genomics, |
RCV004795919 | SCV005418833 | uncertain significance | Polycystic kidney disease, adult type | criteria provided, single submitter | clinical testing | PM2_Supporting+PP3+PS4_Supporting+PP4 | |
Women's Health and Genetics/Laboratory Corporation of America, |
RCV005407351 | SCV006071609 | likely pathogenic | PKD1-Biallelic Autosomal Recessive Polycystic Kidney Disease | 2025-03-14 | criteria provided, single submitter | clinical testing | Variant summary: PKD1 c.6916-10C>A alters a non-conserved nucleotide located at a position not widely known to affect splicing. Several computational tools predict a significant impact on normal splicing: Three predict the variant weakens a 3' acceptor site. One predict the variant no significant impact on splicing. At least one publication reports experimental evidence that this variant affects mRNA splicing (Rossetti_2007). The variant was absent in 166728 control chromosomes. c.6916-10C>A has been reported in the literature in an individual affected with PKD1- Autosomal dominant Polycystic Kidney Disease (Rossetti_2007). The following publication have been ascertained in the context of this evaluation (PMID: 17582161). ClinVar contains an entry for this variant (Variation ID: 3383031). Based on the evidence outlined above, the variant was classified as likely pathogenic. |