Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
ARUP Laboratories, |
RCV001287512 | SCV001474207 | uncertain significance | Polycystic kidney disease, adult type | 2020-04-04 | criteria provided, single submitter | clinical testing | The PKD1 c.7702A>G; p.Arg2568Gly variant, to our knowledge, is not reported in the medical literature or gene specific databases. This variant is also absent from general population databases (Exome Variant Server, Genome Aggregation Database), indicating it is not a common polymorphism. The arginine at codon 2568 is weakly conserved, but computational analyses (SIFT, PolyPhen-2) predict that this variant is deleterious. Due to limited information, the clinical significance of the p.Arg2568Gly variant is uncertain at this time. |
Athena Diagnostics | RCV001664799 | SCV001879454 | uncertain significance | not provided | 2020-11-19 | criteria provided, single submitter | clinical testing | |
Fulgent Genetics, |
RCV001287512 | SCV002777726 | uncertain significance | Polycystic kidney disease, adult type | 2022-02-23 | criteria provided, single submitter | clinical testing | |
Gene |
RCV001664799 | SCV005371410 | uncertain significance | not provided | 2023-06-13 | criteria provided, single submitter | clinical testing | Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; Has not been previously published as pathogenic or benign to our knowledge; This variant is associated with the following publications: (PMID: 37024297) |