Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000483119 | SCV000573131 | uncertain significance | not provided | 2017-02-27 | criteria provided, single submitter | clinical testing | The H2805R variant in the PKD1 gene has not been reported previously as a pathogenic variant, nor as a benign variant, to our knowledge. The H2805R variant is not observed at a significant frequency in large population cohorts (Lek et al., 2016; 1000 Genomes Consortium et al., 2015; Exome Variant Server). The H2805R variant is a conservative amino acid substitution, which is not likely to impact secondary protein structure as these residues share similar properties. This substitution occurs at a position that is not conserved. In silico analysis is inconsistent in its predictions as to whether or not the variant is damaging to the protein structure/function. We interpret H2805R as a variant of uncertain significance. |
Fulgent Genetics, |
RCV002489174 | SCV002793138 | uncertain significance | Polycystic kidney disease, adult type | 2022-03-28 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV005384732 | SCV006045314 | uncertain significance | Inborn genetic diseases | 2025-03-08 | criteria provided, single submitter | clinical testing | The c.8414A>G (p.H2805R) alteration is located in exon 23 (coding exon 23) of the PKD1 gene. This alteration results from a A to G substitution at nucleotide position 8414, causing the histidine (H) at amino acid position 2805 to be replaced by an arginine (R). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |