Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV003154124 | SCV003842538 | pathogenic | not provided | 2023-03-13 | criteria provided, single submitter | clinical testing | Frameshift variant predicted to result in protein truncation or nonsense mediated decay in a gene for which loss-of-function is a known mechanism of disease; Not observed in large population cohorts (gnomAD); This variant is associated with the following publications: (PMID: 17582161, 17574468) |
Prevention |
RCV003928958 | SCV004745336 | pathogenic | PKD1-related disorder | 2024-02-14 | no assertion criteria provided | clinical testing | The PKD1 c.9320_9324dup5 variant is predicted to result in a frameshift and premature protein termination (p.Ile3109Alafs*209). This variant has been reported to be pathogenic for autosomal dominant polycystic kidney disease (ADPKD) (Garcia-Gonzalez et al. 2007. PubMed ID: 17574468, Supplementary Table 1). This variant has not been reported in a large population database (http://gnomad.broadinstitute.org), indicating this variant is rare. Frameshift variants in PKD1 are expected to be pathogenic. This variant is interpreted as pathogenic. |