Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Laboratory of Nephrology, |
RCV002251312 | SCV002520701 | uncertain significance | Polycystic kidney disease, adult type | 2021-10-15 | no assertion criteria provided | clinical testing | This variant was found in a male patient with BBS5 syndrome. This patient presented end stage kidney disease, and CT imaging showed severe atrophy and nephrocystosis of bilateral kidney. However, his mother harboring the same heterozygous variant showed normal renal function and normal CT imaging. |