Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Instituto de Genética, |
RCV002465374 | SCV002600213 | pathogenic | Spondyloepiphyseal dysplasia tarda, X-linked | 2022-11-12 | criteria provided, single submitter | clinical testing | Variant detected in three affected males, detected also in an obligated carrier female. Variant not found in male children of affected individual. |