Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
3billion | RCV002283937 | SCV002573166 | uncertain significance | Severe combined immunodeficiency due to CARMIL2 deficiency | 2022-09-01 | criteria provided, single submitter | clinical testing | The variant is not observed in the gnomAD v2.1.1 dataset. While this variant results in missense change, protein truncation variants are a common disease-causing mechanism. In silico tool predictions suggest damaging effect of the variant on gene or gene product (REVEL: 0.38; 3Cnet: 0.82). Therefore, this variant is classified as uncertain significance according to the recommendation of ACMG/AMP guideline. |