Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Neuberg Centre For Genomic Medicine, |
RCV004818957 | SCV005438965 | uncertain significance | Borjeson-Forssman-Lehmann syndrome | 2023-06-22 | criteria provided, single submitter | clinical testing | The observed missense c.44G>Ap.Arg15His variant in PHF6 gene has not been reported previously as a pathogenic variant nor a benign variant, to our knowledge. The p.Arg15His variant is absent in gnomAD Exomes. This variant has not been submitted to the ClinVar database. Multiple lines of computational evidences Polyphen - Probably damaging, SIFT - Tolerated and MutationTaster - Disease causing predict conflicting evidence on protein structure and function for this variant. The reference amino acid change at this positon on PHF6 gene is predicted as conserved by GERP++ and PhyloP across 100 vertebrates. The amino acid Arg at position 15 is changed to a His changing protein sequence and it might alter its composition and physico-chemical properties. For these reasons, this variant has been classified as a Variant of Uncertain Significance VUS. |