Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Hacettepe Pediatric Genetics Laboratory, |
RCV002464549 | SCV002524164 | uncertain significance | Atypical glycine encephalopathy | 2022-06-08 | no assertion criteria provided | clinical testing | The affected three fetuses exhibited a similar phenotypes including short neck, thoracic kyphosis, hypertrichosis, joint contractures and dislocations, hypertonia, knee hyperextension and facial dysmorphic features. The SLC6A9 variant is classified as “VUS” according to ACMG 2015 criteria and the CADD score was calculated as 27.7. |