Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Mendelics | RCV000990817 | SCV001141862 | pathogenic | Neurodegeneration with brain iron accumulation 5 | 2019-05-28 | criteria provided, single submitter | clinical testing | |
Revvity Omics, |
RCV000990817 | SCV003814802 | likely pathogenic | Neurodegeneration with brain iron accumulation 5 | 2022-07-29 | criteria provided, single submitter | clinical testing | |
3billion | RCV000990817 | SCV003841962 | pathogenic | Neurodegeneration with brain iron accumulation 5 | 2023-02-23 | criteria provided, single submitter | clinical testing | The variant is not observed in the gnomAD v2.1.1 dataset. This variant was predicted to alter splicing and result in a loss or disruption of normal protein function. Multiple pathogenic loss-of-function variants are reported downstream of the variant. The variant has been reported to be associated with WDR45 related disorder (ClinVar ID: VCV000803997). Therefore, this variant is classified as Pathogenic according to the recommendation of ACMG/AMP guideline. |