Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Neuberg Centre For Genomic Medicine, |
RCV004771763 | SCV005382495 | uncertain significance | Arthrogryposis multiplex congenita 2, neurogenic type | 2023-05-20 | criteria provided, single submitter | clinical testing | The observed splice donor variant c.155+1G>A in the ERGIC1 gene has not been reported previously as a pathogenic variant nor as a benign variant, to our knowledge. This variant is reported with the allele frequency 0.004% in the gnomAD Exomes. The variant affects the GT donor splice site downstream of exon 3. Loss of function variants in this gene have not been previously reported to be disease causing. Additional studies are required to prove the pathogenicity of the variant. For these reasons, this variant has been classified as Uncertain significance. |