Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Color Diagnostics, |
RCV001525707 | SCV001735887 | uncertain significance | Cardiomyopathy | 2022-08-29 | criteria provided, single submitter | clinical testing | This missense variant replaces leucine with phenylalanine at codon 3561 of the RYR2 protein. Computational prediction suggests that this variant may have deleterious impact on protein structure and function (internally defined REVEL score threshold >= 0.7, PMID: 27666373). To our knowledge, functional studies have not been reported for this variant. This variant has not been reported in individuals affected with cardiovascular disorders in the literature. This variant has not been identified in the general population by the Genome Aggregation Database (gnomAD). The available evidence is insufficient to determine the role of this variant in disease conclusively. Therefore, this variant is classified as a Variant of Uncertain Significance. |
All of Us Research Program, |
RCV004008867 | SCV004815897 | uncertain significance | Catecholaminergic polymorphic ventricular tachycardia | 2023-02-24 | criteria provided, single submitter | clinical testing | This missense variant replaces leucine with phenylalanine at codon 3561 of the RYR2 protein. Computational prediction suggests that this variant may have deleterious impact on protein structure and function (internally defined REVEL score threshold >= 0.7, PMID: 27666373). To our knowledge, functional studies have not been reported for this variant. This variant has not been reported in individuals affected with cardiovascular disorders in the literature. This variant has not been identified in the general population by the Genome Aggregation Database (gnomAD). The available evidence is insufficient to determine the role of this variant in disease conclusively. Therefore, this variant is classified as a Variant of Uncertain Significance. |
Clinical Genomics Laboratory, |
RCV005051908 | SCV005685439 | uncertain significance | Ventricular arrhythmias due to cardiac ryanodine receptor calcium release deficiency syndrome | 2024-11-19 | criteria provided, single submitter | clinical testing | The RYR2 c.10681C>T (p.Leu3561Phe) variant, to our knowledge, has not been reported in the medical literature and is absent from the general population (gnomAD v.2.1.1), indicating it is not a common variant. Computational predictors indicate that the variant is damaging, evidence that correlates with impact to RYR2 function. Due to limited information, and based on ACMG/AMP guidelines for variant interpretation (Richards S et al., PMID: 25741868), the clinical significance of this variant is uncertain at this time. |