Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Color Diagnostics, |
RCV001188035 | SCV001354980 | uncertain significance | Cardiomyopathy | 2019-12-03 | criteria provided, single submitter | clinical testing | This missense variant replaces glycine with alanine at codon 1235 of the RYR2 protein. Computational prediction tool suggests that this variant may have deleterious impact on protein structure and function (internally defined REVEL score threshold ≥0.7, PMID: 27666373). Splice site prediction tools suggest that this variant may not impact RNA splicing. To our knowledge, functional studies have not been performed for this variant. This variant has not been reported in individuals affected with cardiovascular disorders in the literature. This variant has not been identified in the general population by the Genome Aggregation Database (gnomAD). The available evidence is insufficient to determine the role of this variant in disease conclusively. Therefore, this variant is classified as a Variant of Uncertain Significance. |
Revvity Omics, |
RCV003142111 | SCV003820585 | uncertain significance | not provided | 2021-09-09 | criteria provided, single submitter | clinical testing | |
All of Us Research Program, |
RCV004010254 | SCV004817054 | uncertain significance | Catecholaminergic polymorphic ventricular tachycardia | 2023-03-04 | criteria provided, single submitter | clinical testing | This missense variant replaces glycine with alanine at codon 1235 of the RYR2 protein. Computational prediction tool suggests that this variant may have deleterious impact on protein structure and function (internally defined REVEL score threshold >=0.7, PMID: 27666373). Splice site prediction tools suggest that this variant may not impact RNA splicing. To our knowledge, functional studies have not been performed for this variant. This variant has not been reported in individuals affected with cardiovascular disorders in the literature. This variant has not been identified in the general population by the Genome Aggregation Database (gnomAD). The available evidence is insufficient to determine the role of this variant in disease conclusively. Therefore, this variant is classified as a Variant of Uncertain Significance. |