Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Laboratory for Molecular Medicine, |
RCV000216202 | SCV000272549 | uncertain significance | not specified | 2015-03-02 | criteria provided, single submitter | clinical testing | Variant classified as Uncertain Significance - Favor Benign. The c.-3A>G variant in TRIOBP has not been previously reported in individuals with hearing loss, bu t has been identified in 1/7502 East Asian chromosomes by the Exome Aggregation Consortium (ExAC, http://exac.broadinstitute.org). This variant is located in th e 5'UTR. The nucleotide position at c.-3 is not conserved through species, with many mammals having a G at this position. Although this variant is more likel y to be benign, additional information is needed to fully assess its clinical si gnificance. |
Prevention |
RCV003955278 | SCV004767510 | likely benign | TRIOBP-related disorder | 2019-07-08 | no assertion criteria provided | clinical testing | This variant is classified as likely benign based on ACMG/AMP sequence variant interpretation guidelines (Richards et al. 2015 PMID: 25741868, with internal and published modifications). |