Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Laboratory for Molecular Medicine, |
RCV000222013 | SCV000270949 | likely benign | not specified | 2016-02-07 | criteria provided, single submitter | clinical testing | p.Ile1928Val in exon 16 of TRIOBP: This variant is not expected to have clinical significance due to a lack of conservation across species, including mammals. O f note, Rhesus, crab-eating macaque, baboon, and green monkey have a valine (Val ) at this position. In addition, computational prediction tools do not suggest a high likelihood of impact to the protein. |
Labcorp Genetics |
RCV001853421 | SCV002115118 | uncertain significance | not provided | 2021-08-07 | criteria provided, single submitter | clinical testing | This sequence change replaces isoleucine with valine at codon 1928 of the TRIOBP protein (p.Ile1928Val). The isoleucine residue is weakly conserved and there is a small physicochemical difference between isoleucine and valine. The frequency data for this variant in the population databases is considered unreliable, as metrics indicate poor data quality at this position in the ExAC database. This variant has not been reported in the literature in individuals affected with TRIOBP-related conditions. ClinVar contains an entry for this variant (Variation ID: 228038). Algorithms developed to predict the effect of missense changes on protein structure and function output the following: SIFT: "Tolerated"; PolyPhen-2: "Benign"; Align-GVGD: "Class C0". The valine amino acid residue is found in multiple mammalian species, which suggests that this missense change does not adversely affect protein function. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Gene |
RCV001853421 | SCV003923364 | uncertain significance | not provided | 2024-05-03 | criteria provided, single submitter | clinical testing | In silico analysis indicates that this missense variant does not alter protein structure/function; Has not been previously published as pathogenic or benign to our knowledge |