Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001349439 | SCV001543784 | uncertain significance | Spondylocostal dysostosis 3, autosomal recessive | 2020-07-30 | criteria provided, single submitter | clinical testing | This sequence change replaces serine with isoleucine at codon 44 of the LFNG protein (p.Ser44Ile). The serine residue is weakly conserved and there is a large physicochemical difference between serine and isoleucine. The frequency data for this variant in the population databases is considered unreliable, as metrics indicate insufficient coverage at this position in the ExAC database. This variant has not been reported in the literature in individuals with LFNG-related conditions. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |