Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001912260 | SCV002147079 | uncertain significance | not provided | 2021-08-25 | criteria provided, single submitter | clinical testing | This sequence change replaces valine with methionine at codon 1022 of the SI protein (p.Val1022Met). The valine residue is moderately conserved and there is a small physicochemical difference between valine and methionine. This variant is present in population databases (rs201018248, ExAC 0.01%). This variant has not been reported in the literature in individuals affected with SI-related conditions. Advanced modeling of protein sequence and biophysical properties (such as structural, functional, and spatial information, amino acid conservation, physicochemical variation, residue mobility, and thermodynamic stability) performed at Invitae indicates that this missense variant is expected to disrupt SI protein function. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Fulgent Genetics, |
RCV002482611 | SCV002786462 | uncertain significance | Sucrase-isomaltase deficiency | 2022-03-03 | criteria provided, single submitter | clinical testing |