Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Illumina Laboratory Services, |
RCV000779583 | SCV000916263 | uncertain significance | Neonatal diabetes mellitus with congenital hypothyroidism | 2018-10-25 | criteria provided, single submitter | clinical testing | The GLIS3 c.2129-1G>C variant occurs in a canonical splice site (acceptor) and is therefore predicted to disrupt or distort the normal gene product. A literature search was performed for the gene and cDNA change. No publications were found based on this search. This variant is not found in the 1000 Genomes Project, the Exome Sequencing Project, Exome Aggregation Consortium, or the Genome Aggregation Database in a region of good sequence coverage so the variant is presumed to be rare. Due to the potential impact of splice (acceptor) variants and the lack of clarifying evidence, the c.2129-1G>C is classified as a variant of unknown significance but suspicious for pathogenicity for neonatal diabetes mellitus with congenital hypothyroidism. This variant was observed by ICSL as part of a predisposition screen in an ostensibly healthy population. |