Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001301996 | SCV001491183 | uncertain significance | Neuronal ceroid lipofuscinosis | 2021-08-27 | criteria provided, single submitter | clinical testing | This sequence change falls in intron 4 of the CLN3 gene. It does not directly change the encoded amino acid sequence of the CLN3 protein. It affects a nucleotide within the consensus splice site of the intron. This variant is present in population databases (rs776314679, ExAC 0.02%). This variant has not been reported in the literature in individuals affected with CLN3-related conditions. Variants that disrupt the consensus splice site are a relatively common cause of aberrant splicing (PMID: 17576681, 9536098). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |