Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000408872 | SCV001587081 | pathogenic | Neurofibromatosis, type 1 | 2020-01-15 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. Loss-of-function variants in NF1 are known to be pathogenic (PMID: 10712197, 23913538). This variant has not been reported in the literature in individuals with NF1-related conditions. ClinVar contains an entry for this variant (Variation ID: 369956). The frequency data for this variant in the population databases is considered unreliable, as metrics indicate insufficient coverage at this position in the ExAC database. This sequence change creates a premature translational stop signal (p.Arg5Serfs*19) in the NF1 gene. It is expected to result in an absent or disrupted protein product. |
Bioscientia Institut fuer Medizinische Diagnostik Gmb |
RCV000408872 | SCV000484937 | likely pathogenic | Neurofibromatosis, type 1 | no assertion criteria provided | clinical testing |