Total submissions: 6
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV000132074 | SCV000187138 | uncertain significance | Hereditary cancer-predisposing syndrome | 2016-01-11 | criteria provided, single submitter | clinical testing | The p.G672V variant (also known as c.2015G>T), located in coding exon 18 of the NF1 gene, results from a G to T substitution at nucleotide position 2015. The glycine at codon 672 is replaced by valine, an amino acid with dissimilar properties. Based on data from the NHLBI Exome Sequencing Project (ESP), the T allele has an overall frequency of approximately 0.01% (1/13006) total alleles studied, having been observed in0.01% (1/8600) European American alleles. To date, this alteration has been detected with an allele frequency of approximately 0.002% (greater than 110000 alleles tested) in our clinical cohort. This amino acid position is well conserved in available vertebrate species. In addition, this alteration is predicted to be tolerated by in silico analysis. Since supporting evidence is limited at this time, the clinical significance of p.G672V remains unclear. |
Labcorp Genetics |
RCV000476573 | SCV000542130 | benign | Neurofibromatosis, type 1 | 2023-12-11 | criteria provided, single submitter | clinical testing | |
Genome- |
RCV000476573 | SCV002561979 | uncertain significance | Neurofibromatosis, type 1 | 2022-03-15 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV002415624 | SCV002723669 | likely benign | Hereditary cancer-predisposing syndrome; Cardiovascular phenotype | 2022-05-24 | criteria provided, single submitter | clinical testing | This alteration is classified as likely benign based on a combination of the following: seen in unaffected individuals, population frequency, intact protein function, lack of segregation with disease, co-occurrence, RNA analysis, in silico models, amino acid conservation, lack of disease association in case-control studies, and/or the mechanism of disease or impacted region is inconsistent with a known cause of pathogenicity. |
Gene |
RCV002464122 | SCV002759242 | uncertain significance | not provided | 2022-11-30 | criteria provided, single submitter | clinical testing | In silico analysis supports that this missense variant does not alter protein structure/function; Has not been previously published as pathogenic or benign to our knowledge; This variant is associated with the following publications: (PMID: 25486365) |
Baylor Genetics | RCV003462030 | SCV004198406 | uncertain significance | Juvenile myelomonocytic leukemia | 2023-07-21 | criteria provided, single submitter | clinical testing |