Total submissions: 5
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Laboratory for Molecular Medicine, |
RCV000213889 | SCV000272219 | uncertain significance | not specified | 2019-01-04 | criteria provided, single submitter | clinical testing | proposed classification - variant undergoing re-assessment, contact laboratory |
Labcorp Genetics |
RCV001505732 | SCV001710640 | likely benign | Neurofibromatosis, type 1 | 2024-03-06 | criteria provided, single submitter | clinical testing | |
Gene |
RCV000866659 | SCV002012640 | uncertain significance | not provided | 2021-07-30 | criteria provided, single submitter | clinical testing | Reported as a variant of uncertain significance in an individual with suspected Noonan spectrum disorder in published literature (Witkowski et al., 2020); Not observed at significant frequency in large population cohorts (Lek et al., 2016); In-silico analysis, which includes splice predictors and evolutionary conservation, is inconclusive as to whether the variant alters gene splicing. In the absence of RNA/functional studies, the actual effect of this sequence change is unknown.; This variant is associated with the following publications: (PMID: 32107864) |
Prevention |
RCV004547522 | SCV004111523 | uncertain significance | NF1-related disorder | 2023-04-17 | criteria provided, single submitter | clinical testing | The NF1 c.2410-12T>C variant is predicted to interfere with splicing. This variant was reported as a variant of uncertain significance in an individual with a suspected RASopathy diagnosis (Table S2 - Witkowski et al. 2020. PubMed ID: 32107864). This variant has not been reported in a large population database (http://gnomad.broadinstitute.org), indicating this variant is rare. In ClinVar this variant has conflicting interpretations of pathogenicity of likely benign and uncertain (https://ncbi.nlm.nih.gov/clinvar/variation/229062/). However, the use of computer prediction programs is not equivalent to functional evidence, and therefore the clinical significance of this variant is uncertain. |
Fulgent Genetics, |
RCV005016573 | SCV005646715 | uncertain significance | Neurofibromatosis, familial spinal; Juvenile myelomonocytic leukemia; Neurofibromatosis, type 1; Neurofibromatosis-Noonan syndrome; Café-au-lait macules with pulmonary stenosis | 2024-05-22 | criteria provided, single submitter | clinical testing |