Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV000213998 | SCV000277763 | uncertain significance | Hereditary cancer-predisposing syndrome | 2015-08-12 | criteria provided, single submitter | clinical testing | The c.2851-3delT intronic variant, located in intron 21 of the NF1 gene, results from a deletion of one nucleotide within intron 21 of the NF1 gene. This variant was not reported in population based cohorts in the following databases: Database of Single Nucleotide Polymorphisms (dbSNP), NHLBI Exome Sequencing Project (ESP), and 1000 Genomes Project. In the ESP, this variant was not observed in 6503 samples (13006 alleles) with coverage at this position. To date, this alteration has been detected with an allele frequency of approximately 0.002% (greater than55000 alleles tested) in our clinical cohort.This nucleotide position is not well conserved in available vertebrate species. Using the BDGP and ESEfinder splice site prediction tools, this alteration is not predicted to have any significant effect on this splice acceptor site; however, direct evidence is unavailable.Since supporting evidence for this variant is limited at this time, the clinical significance ofc.2851-3delTremains unclear. |
Labcorp Genetics |
RCV001448764 | SCV001651864 | likely benign | Neurofibromatosis, type 1 | 2024-09-12 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV002433940 | SCV002749875 | likely benign | Hereditary cancer-predisposing syndrome; Cardiovascular phenotype | 2020-03-13 | criteria provided, single submitter | clinical testing | This alteration is classified as likely benign based on a combination of the following: seen in unaffected individuals, population frequency, intact protein function, lack of segregation with disease, co-occurrence, RNA analysis, in silico models, amino acid conservation, lack of disease association in case-control studies, and/or the mechanism of disease or impacted region is inconsistent with a known cause of pathogenicity. |
Baylor Genetics | RCV003469075 | SCV004198985 | uncertain significance | Juvenile myelomonocytic leukemia | 2022-04-11 | criteria provided, single submitter | clinical testing |