Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV002023286 | SCV002306644 | uncertain significance | Neurofibromatosis, type 1 | 2022-08-09 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Advanced modeling of protein sequence and biophysical properties (such as structural, functional, and spatial information, amino acid conservation, physicochemical variation, residue mobility, and thermodynamic stability) performed at Invitae indicates that this missense variant is not expected to disrupt NF1 protein function. ClinVar contains an entry for this variant (Variation ID: 1512957). This variant has not been reported in the literature in individuals affected with NF1-related conditions. This variant is not present in population databases (gnomAD no frequency). This sequence change replaces glutamine, which is neutral and polar, with histidine, which is basic and polar, at codon 1010 of the NF1 protein (p.Gln1010His). |
Ambry Genetics | RCV004558805 | SCV005047658 | uncertain significance | Hereditary cancer-predisposing syndrome; Cardiovascular phenotype | 2023-09-06 | criteria provided, single submitter | clinical testing | The p.Q1010H variant (also known as c.3030A>C), located in coding exon 23 of the NF1 gene, results from an A to C substitution at nucleotide position 3030. The glutamine at codon 1010 is replaced by histidine, an amino acid with highly similar properties. This amino acid position is conserved. In addition, this alteration is predicted to be tolerated by in silico analysis. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
Quest Diagnostics Nichols Institute San Juan Capistrano | RCV004999611 | SCV005624559 | uncertain significance | not provided | 2023-12-06 | criteria provided, single submitter | clinical testing |