Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000557782 | SCV000628486 | pathogenic | Neurofibromatosis, type 1 | 2017-04-22 | criteria provided, single submitter | clinical testing | This sequence change deletes 1 nucleotide from exon 23 of the NF1 mRNA (c.3075delG), causing a frameshift at codon 1026. This creates a premature translational stop signal (p.Arg1026Glufs*10) and is expected to result in an absent or disrupted protein product. While this particular variant has not been reported in the literature, loss-of-function variants in NF1 are known to be pathogenic (PMID: 10712197, 23913538). For these reasons, this variant has been classified as Pathogenic. |