Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Molecular Diagnostics Laboratory, |
RCV000761316 | SCV000891301 | likely pathogenic | Neurofibromatosis, type 1 | 2017-01-11 | criteria provided, single submitter | clinical testing | |
Invitae | RCV000761316 | SCV000955088 | pathogenic | Neurofibromatosis, type 1 | 2018-07-06 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. Loss-of-function variants in NF1 are known to be pathogenic (PMID: 10712197, 23913538). This variant has not been reported in the literature in individuals with NF1-related disease. This variant is not present in population databases (ExAC no frequency). This sequence change creates a premature translational stop signal (p.Leu1418*) in the NF1 gene. It is expected to result in an absent or disrupted protein product. |
Genome- |
RCV000761316 | SCV002560034 | pathogenic | Neurofibromatosis, type 1 | 2022-03-15 | criteria provided, single submitter | clinical testing |