Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV002333518 | SCV002631135 | pathogenic | Hereditary cancer-predisposing syndrome; Cardiovascular phenotype | 2017-08-14 | criteria provided, single submitter | clinical testing | The c.4372_4373delTT pathogenic mutation, located in coding exon 33 of the NF1 gene, results from a deletion of two nucleotides at nucleotide positions 4372 to 4373, causing a translational frameshift with a predicted alternate stop codon (p.F1458Pfs*2). This alteration is expected to result in loss of function by premature protein truncation or nonsense-mediated mRNA decay. As such, this alteration is interpreted as a disease-causing mutation. |