Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000497088 | SCV001229547 | pathogenic | Neurofibromatosis, type 1 | 2019-05-25 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. Loss-of-function variants in NF1 are known to be pathogenic (PMID: 10712197, 23913538). This variant has been observed in an individual affected with neurofibromatosis type 1 (PMID: 28961165). ClinVar contains an entry for this variant (Variation ID: 431645). This variant is not present in population databases (ExAC no frequency). This sequence change creates a premature translational stop signal (p.Leu1486*) in the NF1 gene. It is expected to result in an absent or disrupted protein product. |
Medical Genetics, |
RCV000497088 | SCV000588787 | pathogenic | Neurofibromatosis, type 1 | 2017-02-02 | no assertion criteria provided | clinical testing |